DELAYED DIAGNOSIS OF CONGENITAL ADRENAL-GLAND HYPERPLASIA DUE TO 11-BETA-HYDROXYLASE DEFICIENCY

被引：0

作者：

FOURCADE, L

VANDEWALLE, JP

DENORAY, G

MAFART, B

GRAS, C

TOUZE, JE

机构：

来源：

SEMAINE DES HOPITAUX | 1995年 / 71卷 / 3-4期

关键词：

ADRENAL HYPERPLASIA; CONGENITAL; HYPERTENSION; HYPOKALEMIA; TOMOGRAPHY; X-RAY COMPUTED;

D O I：

暂无

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

11-beta-hydroxylase deficiency is an abnormality of the synthesis of adrenal gland steroids that is usually diagnosed during infancy or childhood. A case diagnosed in a 55-year-old male with severe arterial hypertension and hypokalemia is reported. Hormone assays and computed tomography findings established the diagnosis. Imaging studies showed extensive atheroma lesions. A brief review of the literature was conducted to examine the features of this condition, which is rarely recognized in adulthood.

引用

页码：98 / 101

页数：4

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