PSEUDO ARYLSULFATASE-A DEFICIENCY - BIOSYNTHESIS OF AN ABNORMAL ARYLSULFATASE-A

被引:16
|
作者
AMEEN, M
CHANG, PL
机构
关键词
D O I
10.1016/0014-5793(87)81204-8
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:130 / 134
页数:5
相关论文
共 50 条
  • [31] THE SLOW KINETIC TRANSIENTS OF ARYLSULFATASE-A
    OFAGAIN, C
    BOND, U
    ORSI, BA
    MANTLE, TJ
    BIOCHEMICAL JOURNAL, 1982, 201 (02) : 345 - 352
  • [32] COMPARATIVE BIOCHEMISTRY OF MAMMALIAN ARYLSULFATASE-A AND ARYLSULFATASE-B
    THOMPSON, DB
    DANIEL, WL
    COMPARATIVE BIOCHEMISTRY AND PHYSIOLOGY B-BIOCHEMISTRY & MOLECULAR BIOLOGY, 1988, 90 (04): : 823 - 831
  • [33] THE EFFECT OF PH ON THE KINETICS OF ARYLSULFATASE-A AND ARYLSULFATASE-B
    OFAGAIN, C
    BUTLER, BM
    MANTLE, TJ
    BIOCHEMICAL JOURNAL, 1983, 213 (03) : 603 - 607
  • [34] MULTIPLE SULFATASE DEFICIENCY - DEGRADATION OF ARYLSULFATASE-A AND ARYLSULFATASE-B AFTER ENDOCYTOSIS IN FIBROBLASTS
    STECKEL, F
    HASILIK, A
    VONFIGURA, K
    EUROPEAN JOURNAL OF BIOCHEMISTRY, 1985, 151 (01): : 147 - 152
  • [35] GENOTYPE ASSIGNMENTS IN A FAMILY WITH THE PSEUDO ARYLSULFATASE-A DEFICIENCY TRAIT WITHOUT METACHROMATIC LEUKODYSTROPHY
    KIHARA, H
    MEEK, WE
    FLUHARTY, AL
    PEDIATRIC RESEARCH, 1984, 18 (10) : 1021 - 1022
  • [36] RETINAL-PIGMENT EPITHELIAL DEGENERATION AND ARYLSULFATASE-A DEFICIENCY
    ZLOTOGORA, J
    SCHAAP, T
    BACH, G
    AMERICAN JOURNAL OF OPHTHALMOLOGY, 1981, 92 (01) : 136 - 137
  • [37] CLONING AND EXPRESSION OF HUMAN ARYLSULFATASE-A
    STEIN, C
    GIESELMANN, V
    KREYSING, J
    POHLMANN, R
    SCHMIDT, B
    WAHEED, A
    MEYER, HE
    OBRIEN, J
    VONFIGURA, K
    BIOLOGICAL CHEMISTRY HOPPE-SEYLER, 1988, 369 (09): : 923 - 923
  • [38] METACHROMATIC LEUKODYSTROPHY - TREATMENT WITH ARYLSULFATASE-A
    GREENE, HL
    HUG, G
    SCHUBERT, WK
    ARCHIVES OF NEUROLOGY, 1969, 20 (02) : 147 - &
  • [39] A KM-MUTANT OF ARYLSULFATASE-A
    HARBEN, AM
    KRAWIECKI, N
    MARCUS, R
    HOMMES, FA
    CLINICA CHIMICA ACTA, 1982, 125 (03) : 351 - 354
  • [40] A NEW ELECTROPHORETIC VARIANT OF ARYLSULFATASE-A
    MANOWITZ, P
    FINE, LV
    NORA, R
    CHOKROVERTY, S
    NATHAN, PE
    FAZZARO, JM
    BIOCHEMICAL MEDICINE AND METABOLIC BIOLOGY, 1988, 39 (01): : 117 - 120