REPLACEMENT THERAPY FOR ALPHA-1-ANTITRYPSIN DEFICIENCY ASSOCIATED WITH EMPHYSEMA

被引:551
|
作者
WEWERS, MD
CASOLARO, MA
SELLERS, SE
SWAYZE, SC
MCPHAUL, KM
WITTES, JT
CRYSTAL, RG
机构
[1] NHLBI, PULM BRANCH, BLDG 10, RM 6D03, BETHESDA, MD 20892 USA
[2] NHLBI, BIOMETR RES BRANCH, BETHESDA, MD 20892 USA
来源
NEW ENGLAND JOURNAL OF MEDICINE | 1987年 / 316卷 / 17期
关键词
D O I
10.1056/NEJM198704233161704
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1055 / 1062
页数:8
相关论文
共 50 条
  • [21] A NEW VARIANT OF ALPHA-1-ANTITRYPSIN DEFICIENCY (SIIYAMA) ASSOCIATED WITH PULMONARY-EMPHYSEMA
    TAKABE, K
    SEYAMA, K
    SHINADA, H
    NOUCHI, T
    MIYAHARA, Y
    NUKIWA, T
    MIYAKE, K
    TSUKIMOTO, K
    ICHIOKA, M
    MARUMO, F
    INTERNAL MEDICINE, 1992, 31 (05) : 702 - 707
  • [22] ALPHA-1-ANTITRYPSIN DEFICIENCY ASSOCIATED WITH PANNICULITIS
    HENDRICK, SJ
    SILVERMAN, AK
    SOLOMON, AR
    HEADINGTON, JT
    JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY, 1988, 18 (04) : 684 - 692
  • [23] EMPHYSEMA OF EARLY ONSET ASSOCIATED WITH A COMPLETE DEFICIENCY OF ALPHA-1-ANTITRYPSIN (NULL HOMOZYGOTES)
    COX, DW
    LEVISON, H
    AMERICAN REVIEW OF RESPIRATORY DISEASE, 1988, 137 (02): : 371 - 375
  • [24] Augmentation therapy of alpha-1 antitrypsin deficiency associated emphysema
    Traclet, J.
    Delaval, P.
    Terrioux, P.
    Mornex, J. -F.
    REVUE DES MALADIES RESPIRATOIRES, 2015, 32 (04) : 435 - 446
  • [25] ALPHA-1-ANTITRYPSIN DEFICIENCY AND PULMONARY-EMPHYSEMA - DNA POLYMORPHISM IN THE HUMAN ALPHA-1-ANTITRYPSIN GENE LOCUS
    WOO, SLC
    KIDD, VJ
    CHANDRA, T
    KURACHI, K
    LONG, G
    DAVIE, EW
    AMERICAN JOURNAL OF HUMAN GENETICS, 1982, 34 (06) : A168 - A168
  • [26] ALPHA-1-ANTITRYPSIN DEFICIENCY AND EMPHYSEMA CAUSED BY HOMOZYGOUS INHERITANCE OF NON-EXPRESSING ALPHA-1-ANTITRYPSIN GENES
    GARVER, RI
    MORNEX, JF
    NUKIWA, T
    BRANTLY, M
    COURTNEY, M
    LECOCQ, JP
    CRYSTAL, RG
    NEW ENGLAND JOURNAL OF MEDICINE, 1986, 314 (12): : 762 - 766
  • [27] ALPHA-1-ANTITRYPSIN DEFICIENCY AND PANNICULITIS - PERSPECTIVES ON DISEASE RELATIONSHIP AND REPLACEMENT THERAPY
    PITTELKOW, MR
    SMITH, KC
    DANIEL, WP
    AMERICAN JOURNAL OF MEDICINE, 1988, 84 (6A): : 80 - 86
  • [28] EXPERIENCE WITH REPLACEMENT THERAPY IN THE DESTRUCTIVE LUNG-DISEASE ASSOCIATED WITH SEVERE ALPHA-1-ANTITRYPSIN DEFICIENCY
    GADEK, JE
    CRYSTAL, RG
    AMERICAN REVIEW OF RESPIRATORY DISEASE, 1983, 127 (02): : S45 - S46
  • [29] THE ALPHA-1-ANTITRYPSIN GENE AND EMPHYSEMA
    PERLMUTTER, DH
    PIERCE, JA
    AMERICAN JOURNAL OF PHYSIOLOGY, 1989, 257 (04): : L147 - L162
  • [30] ALPHA-1-ANTITRYPSIN AND THE PATHOGENESIS OF EMPHYSEMA
    STOCKLEY, RA
    LUNG, 1987, 165 (02) : 61 - 77