Tumors of the temporal bone are rare and usually have symptoms such as otorrhea, otalgia and hearing loss and, therefore, can be easily confused with an infectious process delaying diagnosis and worse prognosis. KS, age 7, male. General condition: regular. On examination: conscious, palpable cervical lymph nodes, mobile; palpable mass, painless and property surveying retroauricular left, left deafness and facial paralysis left. Cranial computed tomography showed a lesion of the temporal bone with extension to the middle fossa and posterior skull that enhance with contrast. Performed complementation with radiological MRI brain image which showed uptake, in contrast T1. Incidences in T2, there is edema temporal lobe adjacent to the lesion. Cerebral angiography showed a tumor obstructing the left sigmoid sinus. Patient underwent left radical mastoidectomy with ligation and resection of the left sigmoid sinus resulting in complete lesional resection. Histopathological and immunohistochemical examination compatible with adenocarcinoma. Referred for cancer therapy with chemotherapy and radiation. Death within four months after neurosurgical treatment. Early diagnosis associated with tumor extension carries a better or worse prognosis for patients affected by this disease.