Synchronous brain and intravascular B-cell lymphoma after remission of an adult hemophagocytic syndrome

被引:3
|
作者
Fonseca, Valter R. [1 ,2 ]
Espada, Eduardo [2 ,3 ]
Geraldes, Ruth [2 ,4 ]
Ortiz, Santiago [5 ]
Sousa, Rita [6 ]
Lopez, Dolores [5 ]
Silva, Marisa Teixeira [1 ]
Victorino, Rui [1 ,2 ]
机构
[1] CHLN Hosp Santa Maria, Serv Med 2, Lisbon, Portugal
[2] Univ Lisbon, Fac Med, Inst Mol Med, P-1699 Lisbon, Portugal
[3] CHLN Hosp Santa Maria, Serv Hematol & Transplantacao Medula, Lisbon, Portugal
[4] CHLN Hosp Santa Maria, Serv Neurol, Lisbon, Portugal
[5] CHLN Hosp Santa Maria, Serv Anat Patol, Lisbon, Portugal
[6] CHLN Hosp Santa Maria, Serv Imagiol Neurol, Lisbon, Portugal
来源
CLINICAL CASE REPORTS | 2016年 / 4卷 / 04期
关键词
Brain lymphoma; hemophagocitic lymphohistiocytosis; intravascular lymphoma; white matter abnormalities;
D O I
10.1002/ccr3.507
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Key Clinical Message Hemophagocytic lymphohistiocytosis (HLH) should be considered in the differential diagnosis of adult patients with white matter disease. Brain involvement can be life-threatening and should prompt aggressive therapy. Even after HLH remission, the possibility of subsequent deterioration due to emergence of an aggressive intravascular lymphoma is highlighted here.
引用
收藏
页码:327 / 330
页数:4
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