Multiorgan staphylococcal infection in a child with hyper-IgE syndrome

被引:0
|
作者
Szygula-Kotala, Ewa [1 ]
Sada-Cieslar, Magdalena [1 ]
Buszman, Zofia [1 ]
机构
[1] Chorzowskie Centrum Pediatr Onkol, Oddzial Alergol Immunol DzieciQcej, ChorzOw, Poland
来源
ALERGIA ASTMA IMMUNOLOGIA | 2006年 / 11卷 / 02期
关键词
hiper-IgE syndrome;
D O I
暂无
中图分类号
R392 [医学免疫学]; Q939.91 [免疫学];
学科分类号
100102 ;
摘要
Hyper-IgE syndrome (Job syndrome, hyperIgE recurrent infection syndrome), a rare imunodeficiency, is characterized by recurrent skin and pulmonary abscesses, pneumonia with formation of pneumatoceles, recurrent eczematoid rashes, typical constitutional traits, as well as extremely high serum IgE levels. A case of a 2,5 year old boy with a Job syndrome and with the symptoms of eczematoid rashes, pneumonia and staphylococcal sepsis has been reported.
引用
收藏
页码:109 / 112
页数:4
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