Unilateral lung agenesis associated with esophageal atresia & tracheoesophageal fistula: Report of two cases & review of literature

被引:3
|
作者
Parelkar, Sandesh V. [1 ]
Athawale, Hemangi R. [1 ]
Sanghvi, Beejal V. [1 ]
Joshi, Prashant B. [1 ]
Kapadnis, Satish P. [1 ]
Oak, Sanjay N. [1 ]
机构
[1] King Edward Mem Hosp, Dept Paediat Surg, E Borges Rd, Bombay 400012, Maharashtra, India
关键词
Lung agenesis; Esophageal atresia (EA); Tracheoesophageal fistula (TEF);
D O I
10.1016/j.epsc.2013.06.003
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
The association of lung agenesis with esophageal atresia ( EA) & tracheoesophageal fistula (TEF) is exceedingly rare with a lethal outcome. We describe two neonates with this association who underwent primary repair shortly after birth. One of these neonates also had gross hydrocephalus, bilateral microtia and right thumb deformity. The goal in the management of these patients is early protection and preservation of respiratory units which is best accomplished by primary repair. (C) 2013 The Authors. Published by Elsevier Inc.
引用
收藏
页码:203 / 206
页数:4
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