ACQUIRED C1-INHIBITOR DEFICIENCY WITH LYMPHOMA CAUSING RECURRENT ANGIOEDEMA

被引：18
|
作者：
MATHUR, R [1 ]
TOGHILL, PJ [1 ]
JOHNSTON, IDA [1 ]
机构：
[1] UNIV NOTTINGHAM HOSP,NOTTINGHAM NG7 2UH,ENGLAND
来源：
POSTGRADUATE MEDICAL JOURNAL | 1993年 / 69卷 / 814期
关键词：
D O I：
10.1136/pgmj.69.814.646
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
A 52 year old man who developed recurrent massive and generalized angioedema for the first time during adult life was found to have an acquired deficiency of Clq esterase inhibitor (C1 INH) in association with a B cell lymphoma producing a paraprotein. He had low levels of C4 and C1 INH during the attacks which returned to normal after the successful treatment of lymphoma. An underlying lymphoproliferative disease should always be considered in adult patients with this immunological profile, recurrent angioedema and a negative family history.
引用
收藏
页码：646 / 648
页数：3
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