Two cases of pancreatic neuroendocrine tumors with ectopic ACTH syndrome during their disease course

被引:0
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作者
Masatoshi Murakami
Keisuke Hirahata
Nao Fujimori
Takeo Yamamoto
Yoshinao Oda
Shingo Kozono
Keijiro Ueda
Testuhide Ito
Masafumi Nakamura
Yoshihiro Ogawa
机构
[1] Kyushu University,Department of Medicine and Bioregulatory Science, Graduate School of Medical Sciences
[2] Kyushu University,Department of Anatomic Pathology, Pathological Sciences, Graduate School of Medical Sciences
[3] Kitakyushu Municipal Medical Center,Department of Surgery
[4] Fukuoka Sanno Hospital,Neuroendocrine Tumor Centre
[5] International University of Health and Welfare,Department of Gastroenterology, Graduate School of Medical Sciences
[6] Kyushu University,Department of Surgery and Oncology, Graduate School of Medical Sciences
来源
关键词
Pancreatic neuroendocrine tumor; Ectopic ACTH syndrome; Cushing’s syndrome; PTHrP; Secondary hormone secretion;
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摘要
Pancreatic neuroendocrine tumors (PanNETs) are rare malignant tumors that occur in the pancreas. They are divided into functioning and non-functioning tumors based on the presence or absence of their specific hormonal hyper-expression symptoms. Adrenocorticotropic hormone (ACTH)-producing PanNETs are rare, functional tumors, and their clinical characteristics and outcomes have not been well reported.
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页码:363 / 370
页数:7
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