Sildenafil in pulmonary hypertension secondary to unilateral agenesis of pulmonary artery

被引:6
|
作者
Hamdan M.A. [1 ,3 ]
Abu-Sulaiman R.M. [1 ]
Najm H.K. [2 ]
机构
[1] Section of Pediatric Cardiology, King Abdulaziz Cardiac Center, King Fahad National Guard Hospital, Riyadh
[2] Section of Cardiovascular Surgery, King Abdulaziz Cardiac Center, King Fahad National Guard Hospital, Riyadh
[3] Tawam Hospital, Al Ain, Abu Dhabi
关键词
Pulmonary artery agensis; Pulmonary hypertension; Sildenafil;
D O I
10.1007/s00246-005-1100-7
中图分类号
学科分类号
摘要
Unilateral agenesis of the pulmonary artery (PA) is a rare anomaly that can lead to pulmonary hypertension (PHTN). We report the case of a 10-month-old female with agenesis of the left PA, ventricular septal defect, and patent ductus arteriosus who developed PHTN precluding surgical repair. The use of sildenafil decreased PA pressure and normalized pulmonary vascular resistance, after which surgery was successfully performed. © Springer Science+Business Media, Inc. 2006.
引用
收藏
页码:279 / 281
页数:2
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