Scimitar Syndrome: A Rare Cause of Dyspnea in Adults

被引:6
|
作者
Yehia, Baligh R. [1 ]
Bachmann, Justin M.
Traill, Thomas A.
机构
[1] Univ Penn, Sch Med, Dept Med, Philadelphia, PA 19104 USA
关键词
anomalous pulmonary venous return; cardiac defects; scimitar syndrome; PULMONARY VENOUS DRAINAGE; INFERIOR VENA-CAVA; RIGHT LUNG; CLINICAL SPECTRUM;
D O I
10.1097/SMJ.0b013e3181dfd59e
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Scimitar syndrome is a rare congenital malformation resulting in anomalous pulmonary venous return and lung malformations. Symptoms commonly develop in the first year of life, leading to diagnosis and surgical correction. In this case, the atypical presentation of scimitar syndrome in an adult woman with complaints of dyspnea on exertion is reported. Although uncommon, congenital conditions should be considered in patients who present with dyspnea and an abnormal chest radiograph.
引用
收藏
页码:578 / 580
页数:3
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