Tetrahydrobiopterin (BH4):: Cofactor for dopamine β hydroxylase (DβH).

被引:0
|
作者
Dashman, T [1 ]
Samuels, S [1 ]
Leshinsky-Silver, E [1 ]
Kolodny, E [1 ]
Axelrod, F [1 ]
机构
[1] NYU, Med Ctr, New York, NY 10016 USA
来源
FASEB JOURNAL | 1997年 / 11卷 / 09期
关键词
D O I
暂无
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
2652
引用
收藏
页码:A1311 / A1311
页数:1
相关论文
共 50 条
  • [1] THE TREATMENT OF PHENYLALANINE HYDROXYLASE (PAH)-DEFICIENT BH4-RESPONSIVE PATIENTS WITH TETRAHYDROBIOPTERIN (BH4): TOLERANCE TO PHE AND RESPONSE TO BH4
    Leuzzi, V.
    Carducci, C.
    De Leo, S.
    Montieri, P.
    Carducci, C.
    Antonozzi, I.
    JOURNAL OF INHERITED METABOLIC DISEASE, 2005, 28 : 33 - 33
  • [2] DIHYDROBIOPTERIN DEFICIENCY - MONOTHERAPY WITH TETRAHYDROBIOPTERIN (BH4) AND DIACETYL BH4
    ENDRES, W
    NIEDERWIESER, A
    CURTIUS, HC
    OHRT, B
    SCHAUB, J
    PEDIATRIC RESEARCH, 1982, 16 (08) : 694 - 694
  • [3] Treatment of ADHD with tetrahydrobiopterin (BH4).
    Matalon, R.
    Bhatia, G.
    Michals-Matalon, K.
    Zinser, W.
    Tyring, S.
    MOLECULAR GENETICS AND METABOLISM, 2008, 93 (03) : 256 - 256
  • [4] Long term tetrahydrobiopterin (BH4) treatment of phenylalanine hydroxylase (PAH) deficient patients
    Leuzzi, V
    De Leo, S.
    Carducci, C., I
    Carducci, C. A.
    Artiola, C.
    Santagata, S.
    Antonozzi, I
    JOURNAL OF INHERITED METABOLIC DISEASE, 2008, 31 : 84 - 84
  • [5] Tetrahydrobiopterin(BH4)-responsiveness and long-term treatment with BH4 in hyperphenylalaninemia
    Scala, I
    Ungaro, C.
    Paladino, S.
    Nastasi, A.
    Zuppaldi, A.
    Sibilio, M.
    Figliuolo, C.
    Scarpato, E.
    Capaldo, B.
    Cardillo, G.
    Daniele, A.
    Della Casa, R.
    Parenti, G.
    Andria, A.
    JOURNAL OF INHERITED METABOLIC DISEASE, 2008, 31 : 82 - 82
  • [6] MOLECULAR CHARACTERIZATION TO PREDICT TETRAHYDROBIOPTERIN (BH4) RESPONSIVENESS IN PHENYLALANINE HYDROXYLASE (PAH) DEFICIENCY
    Bettocchi, I
    Nicoletti, A.
    Baronio, F.
    Monti, S.
    Rizzello, A.
    Baldazzi, L.
    Cassio, A.
    Pession, A.
    Bal, M. O.
    JOURNAL OF INHERITED METABOLIC DISEASE, 2012, 35 : S34 - S34
  • [7] The eNOS cofactor tetrahydrobiopterin (BH4) improves endothelial dysfunction of CCL4 cirrhotic livers
    Matei, V
    Deulofeu, R
    Rodriguez-Vilarupla, A
    Bosch, J
    Garcia-Pagán, JC
    HEPATOLOGY, 2004, 40 (04) : 728A - 728A
  • [8] Glucocorticoid-Induced Hypertension and Tetrahydrobiopterin (BH4), a Common Cofactor for the Production of Vasoactive Molecules
    Mitchell, Brett M.
    Webb, Clinton
    CURRENT HYPERTENSION REVIEWS, 2005, 1 (01) : 1 - 6
  • [9] TETRAHYDROBIOPTERIN (BH4) AND MATERNAL PHENYLKETONURIA (PKU)
    Koch, R.
    Moseley, K.
    Guttler, F.
    JOURNAL OF INHERITED METABOLIC DISEASE, 2005, 28 : 30 - 30
  • [10] Cuticle Integrity and Biogenic Amine Synthesis in Caenorhabditis elegans Require the Cofactor Tetrahydrobiopterin (BH4)
    Loer, Curtis M.
    Calvo, Ana C.
    Watschinger, Katrin
    Werner-Felmayer, Gabriele
    O'Rourke, Delia
    Stroud, Dave
    Tong, Amy
    Gotenstein, Jennifer R.
    Chisholm, Andrew D.
    Hodgkin, Jonathan
    Werner, Ernst R.
    Martinez, Aurora
    GENETICS, 2015, 200 (01) : 237 - U457