Distinct liquid-like properties of axonal TDP-43 RNP granules

被引:0
|
作者
Gopal, Pallavi [1 ]
Nirschl, Jeffrey [1 ]
Klinman, Eva [1 ]
Holzbaur, Erika [1 ]
机构
[1] Univ Penn, Philadelphia, PA 19104 USA
关键词
D O I
暂无
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
118
引用
收藏
页码:600 / 600
页数:1
相关论文
共 50 条
  • [1] ALS-Linked Mutations Increase the Viscosity of Liquid-Like Axonal TDP-43 RNP Granules in Neurons
    Gopal, Pallavi P.
    Nirschl, Jeffrey J.
    Klinman, Eva
    Holzbaur, Erika L. F.
    ANNALS OF NEUROLOGY, 2017, 82 : S212 - S212
  • [2] ALS-linked mutations increase the viscosity of liquid-like axonal TDP-43 RNP granules in neurons.
    Gopal, P. P.
    Nirschl, J. J.
    Klinman, E.
    Holzbaur, E. L.
    MOLECULAR BIOLOGY OF THE CELL, 2017, 28
  • [3] ALS-linked mutations increase the viscosity of liquid-like axonal TDP-43 RNP granules in neurons.
    Gopal, P. P.
    Nirschl, J. J.
    Klinman, E.
    Holzbaur, E. L.
    MOLECULAR BIOLOGY OF THE CELL, 2016, 27
  • [4] Amyotrophic lateral sclerosis-linked mutations increase the viscosity of liquid-like TDP-43 RNP granules in neurons
    Gopal, Pallavi P.
    Nirschl, Jeffrey J.
    Klinman, Eva
    Holzbaur, Erika L. F.
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 2017, 114 (12) : E2466 - E2475
  • [5] Amyotrophic lateral sclerosis-linked mutations increase the viscosity of liquid-like TDP-43 RNP granules in neurons
    Gopal, Pallavi
    Nirschl, Jeffrey
    Klinman, Eva
    Holzbaur, Erika
    JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 2017, 76 (06): : 519 - 519
  • [6] Axonal Transport of TDP-43 mRNA Granules Is Impaired by ALS-Causing Mutations
    Alami, Nael H.
    Smith, Rebecca B.
    Carrasco, Monica A.
    Williams, Luis A.
    Winborn, Christina S.
    Han, Steve S. W.
    Kiskinis, Evangelos
    Winborn, Brett
    Freibaum, Brian D.
    Kanagaraj, Anderson
    Clare, Alison J.
    Badders, Nisha M.
    Bilican, Bilada
    Chaum, Edward
    Chandran, Siddharthan
    Shaw, Christopher E.
    Eggan, Kevin C.
    Maniatis, Tom
    Taylor, J. Paul
    NEURON, 2014, 81 (03) : 536 - 543
  • [7] Hsp70 chaperones TDP-43 in dynamic, liquid-like phase and prevents it from amyloid aggregation
    Gu, Jinge
    Wang, Chen
    Hu, Rirong
    Li, Yichen
    Zhang, Shengnan
    Sun, Yunpeng
    Wang, Qiangqiang
    Li, Dan
    Fang, Yanshan
    Liu, Cong
    CELL RESEARCH, 2021, 31 (09) : 1024 - 1027
  • [8] Prion-like properties of assembled TDP-43
    Nonaka, Takashi
    Hasegawa, Masato
    CURRENT OPINION IN NEUROBIOLOGY, 2020, 61 : 23 - 28
  • [9] Hsp70 chaperones TDP-43 in dynamic, liquid-like phase and prevents it from amyloid aggregation
    Jinge Gu
    Chen Wang
    Rirong Hu
    Yichen Li
    Shengnan Zhang
    Yunpeng Sun
    Qiangqiang Wang
    Dan Li
    Yanshan Fang
    Cong Liu
    Cell Research, 2021, 31 : 1024 - 1027
  • [10] Colocalization of TDP-43 and stress granules at the early stage of TDP-43 aggregation in amyotrophic lateral sclerosis
    Mori, Fumiaki
    Yasui, Hina
    Miki, Yasuo
    Kon, Tomoya
    Arai, Akira
    Kurotaki, Hidekachi
    Tomiyama, Masahiko
    Wakabayashi, Koichi
    BRAIN PATHOLOGY, 2024, 34 (02)