Renal lymphangiomatosis is an unusual disorder. It may develop due to the abnormality of the intrarenal, peripelvic and perirenal lymphatics. The differential diagnosis contains renal lymphoma, polycystic kidney disease, multicystic dysplasia and renal tumors. We report a case of renal lymphangiomatosis, previously diagnosed as autosomal dominant polycystic kidney disease, to emphasize that these two diseases can be easily confused. It should be kept in mind that RL is in the differential diagnosis of polycystic renal disease to prevent overtreatment.
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Univ Tokyo, Grad Sch Med, Dept Urol, Bunkyo Ku, 7-3-1 Hongo, Tokyo 1138654, JapanUniv Tokyo, Grad Sch Med, Dept Urol, Bunkyo Ku, 7-3-1 Hongo, Tokyo 1138654, Japan
Hakozaki, Yuji
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Uchiyama, Kiyotaka
Yanai, Akane
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Japanese Red Cross Med Ctr, Div Nephrol, Shibuya Ku, 4-1-22 Hiroo, Tokyo 1508935, JapanUniv Tokyo, Grad Sch Med, Dept Urol, Bunkyo Ku, 7-3-1 Hongo, Tokyo 1138654, Japan
Yanai, Akane
Yamada, Daisuke
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St Lukes Int Hosp, Dept Radiol, Chuo Ku, 9-1 Akashi Cho, Tokyo 1048560, JapanUniv Tokyo, Grad Sch Med, Dept Urol, Bunkyo Ku, 7-3-1 Hongo, Tokyo 1138654, Japan
Yamada, Daisuke
Kamijo, Yuka
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Japanese Red Cross Med Ctr, Div Nephrol, Shibuya Ku, 4-1-22 Hiroo, Tokyo 1508935, JapanUniv Tokyo, Grad Sch Med, Dept Urol, Bunkyo Ku, 7-3-1 Hongo, Tokyo 1138654, Japan
Kamijo, Yuka
Ishibashi, Yoshitaka
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Japanese Red Cross Med Ctr, Div Nephrol, Shibuya Ku, 4-1-22 Hiroo, Tokyo 1508935, JapanUniv Tokyo, Grad Sch Med, Dept Urol, Bunkyo Ku, 7-3-1 Hongo, Tokyo 1138654, Japan
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Brigham & Womens Hosp, 75 Francis St, Boston, MA 02115 USA
Brigham & Womens Hosp, Surg Educ, CA 034,75 Francis St, Boston, MA 02115 USABrigham & Womens Hosp, 75 Francis St, Boston, MA 02115 USA
Gomez, Gricelda
Althaus, Adam
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Brigham & Womens Hosp, 75 Francis St, Boston, MA 02115 USABrigham & Womens Hosp, 75 Francis St, Boston, MA 02115 USA
Althaus, Adam
Gruessner, Christine E.
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Brigham & Womens Hosp, 75 Francis St, Boston, MA 02115 USABrigham & Womens Hosp, 75 Francis St, Boston, MA 02115 USA
Gruessner, Christine E.
Hirsch, Michelle S.
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Brigham & Womens Hosp, 75 Francis St, Boston, MA 02115 USABrigham & Womens Hosp, 75 Francis St, Boston, MA 02115 USA
Hirsch, Michelle S.
Steele, Graeme S.
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Brigham & Womens Hosp, 75 Francis St, Boston, MA 02115 USABrigham & Womens Hosp, 75 Francis St, Boston, MA 02115 USA