Thrombotic microangiopathy with liver, gut, and bone infarction (catastrophic antiphospholipid syndrome) associated with HELLP syndrome

被引：37
|
作者：
Koenig, M [1 ]
Roy, M
Baccot, S
Cuilleron, M
de Filippis, JP
Cathébrasl, P
机构：
[1] CHU St Etienne, Hop Nord, Dept Internal Med, F-42055 St Etienne, France
[2] CHU St Etienne, Hop Nord, Dept Gen Surg, F-42055 St Etienne, France
[3] CHU St Etienne, Hop Nord, Dept Radiol, F-42055 St Etienne, France
[4] CHU St Etienne, Hop Nord, Dept Nephrol, F-42055 St Etienne, France
来源：
CLINICAL RHEUMATOLOGY | 2005年 / 24卷 / 02期
关键词：
bone infarction; HELLP syndrome; pregnancy; primary antiphospholipid syndrome; thrombotic microangiopathy;
D O I：
10.1007/s10067-004-1017-1
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Hemolysis, elevated liver enzymes, low platelet count (HELLP) syndrome is a thrombotic microangiopathy complicating pregnancy and shares many clinical and biological features with thrombotic thrombocytopenic purpura (TTP) and hemolytic uremic syndrome (HUS). Thrombotic microangiopathy is also a pathological feature of catastrophic antiphospholipid syndrome (CAPS). An association between refractory HELLP syndrome and antiphospholipid syndrome (APS) has been reported in a few cases. We describe a 19-year-old woman with APS and multiorgan failure conforming to a diagnosis of CAPS who developed refractory HELLP syndrome.
引用
收藏
页码：166 / 168
页数：3
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