Hepatocellular carcinoma in a child with Niemann-Pick disease: Imaging findings

被引:9
|
作者
Pennington, DJ
Sivit, CJ
Chandra, RS
机构
[1] CHILDRENS NATL MED CTR,DEPT DIAGNOST IMAGING & RADIOL,WASHINGTON,DC 20010
[2] CHILDRENS NATL MED CTR,DEPT PEDIAT,WASHINGTON,DC 20010
[3] CHILDRENS NATL MED CTR,DEPT PATHOL,WASHINGTON,DC 20010
[4] GEORGE WASHINGTON UNIV,SCH MED & HLTH SCI,WASHINGTON,DC 20052
关键词
D O I
10.1007/BF01405304
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Niemann-Pick disease (NPD) is a metabolic disease in which cirrhosis is relatively common; however, there is no known association of NPD with hepatocellular carcinoma. We present a case of metastatic, multifocal hepatocellular carcinoma in a 4-year-old boy with NPD and onset of cirrhosis in infancy.
引用
收藏
页码:220 / 221
页数:2
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