Spontaneous dural tear leading to intracranial hypotension and tonsillar herniation in Marfan syndrome: a case report

被引：12
|
作者：
Pabaney, Aqueel H. [2 ]
Mirza, Farhan A. [1 ]
Syed, Nadir A. [2 ]
Ahsan, Humera [3 ]
机构：
[1] Aga Khan Univ Hosp, Coll Med, Karachi, Pakistan
[2] Aga Khan Univ Hosp, Dept Neurol, Karachi, Pakistan
[3] Aga Khan Univ Hosp, Dept Neuroradiol, Karachi, Pakistan
来源：
BMC NEUROLOGY | 2010年 / 10卷
关键词：
CEREBROSPINAL-FLUID LEAKS; SECONDARY; HEADACHE; ENHANCEMENT; PATIENT;
D O I：
10.1186/1471-2377-10-54
中图分类号：
R74 [神经病学与精神病学];
学科分类号：
摘要：
Background: We describe the case of a 38 year old male with Marfan syndrome who presented with orthostatic headaches and seizures. Case Presentation: The patient was diagnosed with Spontaneous Intracranial Hypotension secondary to CSF leaks, objectively demonstrated by MR Myelogram with intrathecal contrast. Epidural autologus blood patch was administered at the leakage site leading to significant improvement. Conclusion: Our literature search shows that this is the second reported case of a Marfan patient presenting with symptomatic spontaneous CSF leaks along with tonsillar herniation.
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页数：4
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