Involvement of the Peripheral Nervous System in Polyarteritis Nodosa and Antineutrophil Cytoplasmic Antibodies-Associated Vasculitis

被引:22
|
作者
Imboden, John B. [1 ]
机构
[1] Univ Calif San Francisco, Dept Med, Box 0868, San Francisco, CA 94143 USA
关键词
Antineutrophil cytoplasmic antibodies (ANCA); Granulomatosis with polyangiitis; Microscopic polyangiitis; Eosinophilic granulomatosis with polyangiitis (Churg-Strauss syndrome); Polyarteritis nodosa; Mononeuritis multiplex; Ischemic neuropathy; CHURG-STRAUSS-SYNDROME; MICROSCOPIC POLYANGIITIS; MONONEURITIS MULTIPLEX; NEUROPATHY; GRANULOMATOSIS; CLASSIFICATION; DIAGNOSIS; UPDATE;
D O I
10.1016/j.rdc.2017.06.011
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Peripheral nerve involvement is common in polyarteritis nodosa and the antineutrophil cytoplasmic antibody (ANCA)-associated vasculitides. The underlying mechanism is arteritis of the vasa nervorum, leading to ischemic neuropathy. The classic presentation is stepwise involvement of peripheral nerves with ongoing antecedent constitutional symptoms. This article reviews the pathologic findings, clinical syndromes, diagnosis, and treatment of ANCA-associated vasculitides.
引用
收藏
页码:633 / +
页数:8
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