Pyruvate Dehydrogenase Complex Deficiency Caused by the Ubiquitin-Proteasome System-Mediated Degradation in E1β Subunit

被引：0
|
作者：
Han, Zongchao
Srivastava, Arun
Stacpoole, Peter
机构：
[1] Univ Florida, Div Cellular & Mol Therapy, Coll Med, Alachua, FL USA
[2] Univ Florida, Coll Med, Gainesville, FL USA
[3] Univ Florida, Coll Med, Gen Clin Res Ctr, Gainesville, FL USA
来源：
MOLECULAR THERAPY | 2006年 / 13卷
关键词：
D O I：
10.1016/j.ymthe.2006.08.249
中图分类号：
Q81 [生物工程学（生物技术）]; Q93 [微生物学];
学科分类号：
071005 ; 0836 ; 090102 ; 100705 ;
摘要：
224
引用
收藏
页码：S86 / S86
页数：1
相关论文
共 50 条
  • [1] Pyruvate dehydrogenase complex deficiency caused by ubiquitination and proteasome-mediated degradation of the E1β subunit
    Han, Zongchao
    Zhong, Li
    Srivastava, Arun
    Stacpoole, Peter W.
    JOURNAL OF BIOLOGICAL CHEMISTRY, 2008, 283 (01) : 237 - 243
  • [2] Regulation of ubiquitin-proteasome system-mediated degradation by cytosolic stress
    Kelly, Sean M.
    VanSlyke, Judy K.
    Musil, Linda S.
    MOLECULAR BIOLOGY OF THE CELL, 2007, 18 (11) : 4279 - 4291
  • [3] Deficiency of pyruvate dehydrogenase caused by novel and known mutations in the E1α subunit
    Cameron, JM
    Levandovskiy, V
    MacKay, N
    Tein, I
    Robinson, BH
    AMERICAN JOURNAL OF MEDICAL GENETICS PART A, 2004, 131A (01) : 59 - 66
  • [4] Mechanisms of expression of pyruvate dehydrogenase deficiency caused by an E1α subunit mutation
    Morten, KJ
    Caky, M
    Matthews, PM
    NEUROLOGY, 1998, 51 (05) : 1324 - 1330
  • [5] Pyruvate dehydrogenase E1 beta subunit deficiency
    Brown, G
    Brown, R
    Head, R
    Boubriak, I
    Leonard, J
    Thomas, N
    BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS, 2004, 1657 : 11 - 12
  • [6] Prefoldin Subunits Are Protected from Ubiquitin-Proteasome System-mediated Degradation by Forming Complex with Other Constituent Subunits
    Miyazawa, Makoto
    Tashiro, Erika
    Kitaura, Hirotake
    Maita, Hiroshi
    Suto, Hiroo
    Iguchi-Ariga, Sanae M. M.
    Ariga, Hiroyoshi
    JOURNAL OF BIOLOGICAL CHEMISTRY, 2011, 286 (22) : 19191 - 19203
  • [7] Pyruvate dehydrogenase deficiency: The relation of the E1 alpha mutation to the E1 beta subunit deficiency
    Fujii, T
    Alvarez, MBG
    Sheu, KFR
    KranzEble, PJ
    DeVivo, DC
    PEDIATRIC NEUROLOGY, 1996, 14 (04) : 328 - 334
  • [8] Folding and assembly defects of pyruvate dehydrogenase deficiency-related variants in the E1α subunit of the pyruvate dehydrogenase complex
    Drakulic, Srdja
    Rai, Jay
    Petersen, Steen Vang
    Golas, Monika M.
    Sander, Bjoern
    CELLULAR AND MOLECULAR LIFE SCIENCES, 2018, 75 (16) : 3009 - 3026
  • [9] Folding and assembly defects of pyruvate dehydrogenase deficiency-related variants in the E1α subunit of the pyruvate dehydrogenase complex
    Srdja Drakulic
    Jay Rai
    Steen Vang Petersen
    Monika M. Golas
    Bjoern Sander
    Cellular and Molecular Life Sciences, 2018, 75 : 3009 - 3026
  • [10] The Role and Mechanisms of Ubiquitin-Proteasome System-Mediated Ferroptosis in Neurological Disorders
    Liu, Xin
    Wang, Wei
    Nie, Qiucheng
    Liu, Xinjing
    Sun, Lili
    Ma, Qiang
    Zhang, Jie
    Wei, Yiju
    NEUROSCIENCE BULLETIN, 2025,
12345