This report describes a transient hypertrophic cardiomyopathy with right-ventricle outlet tract obstruction (RVOTO) induced by perinatal stress due to a major surgical procedure in a female newborn with congenital abnormalities. On day 10, she presented with heart failure, abnormal B-type natriuretic peptide (BNP), and an echocardiogram showing normal wall thickness. An in-hospital follow-up echocardiogram showed biventricular hypertrophy and RVOTO. At discharge, the infant was asymptomatic, with a normal echocardiogram and BNP. Transient RVOTO triggered by surgical stress and abnormal BNP have not been reported previously. Pathophysiology, the role of BNP, and clinical characteristics are discussed.
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Great Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, EnglandGreat Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, England
Kaski, J. P.
Esteban, M. T. Tome
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Great Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, EnglandGreat Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, England
Esteban, M. T. Tome
Mead-Regan, S.
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Great Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, EnglandGreat Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, England
Mead-Regan, S.
Pantazis, A.
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Great Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, EnglandGreat Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, England
Pantazis, A.
Marek, J.
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Great Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, EnglandGreat Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, England
Marek, J.
Deanfield, J. E.
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Great Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, EnglandGreat Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, England
Deanfield, J. E.
McKenna, W. J.
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Great Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, EnglandGreat Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, England
McKenna, W. J.
Elliott, P. M.
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Great Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, EnglandGreat Ormond St Hosp Sick Children, Dept Cardiol, Inherited Cardiovasc Dis Unit, London, England