Primary paratesticular embryonal rhabdomyosarcoma - An unusual presentation

被引:0
|
作者
Singh, Priyanka [1 ]
Anandani, Garima [2 ,3 ]
Parmar, Riddhi [2 ]
机构
[1] VMMC & Safdarjung Hosp, Dept Pathol, New Delhi, India
[2] All India Inst Med Sci AIIMS, Dept Pathol, Rajkot, Gujarat, India
[3] Dept Pathol, 212 AIIMS Rajkot Permanent Campus, Rajkot 360110, Gujarat, India
关键词
Metastasis; paratesticular mass; rhabdomyosarcoma; DIAGNOSIS; MASSES;
D O I
10.4103/jfmpc.jfmpc_397_23
中图分类号
R1 [预防医学、卫生学];
学科分类号
1004 ; 120402 ;
摘要
Paratesticular embryonal rhabdomyosarcoma (RMS) is a very rare and aggressive mesenchymal tumor. It is usually seen in children and adolescents presenting as a painless intrascrotal mass, localized in the paratesticular region. Hereby, we report two cases of paratesticular embryonal RMS in adults. One case was clinically suspected to be a testicular abscess, whereas the other presented with testicular swelling and lung metastasis. Localized forms have a good prognosis, whereas tumors presenting with metastases show a poor outcome. A treatment based on surgery and chemotherapy yields good results. Sperm cryopreservation and endocrine follow-up improve the overall survival and quality of life of these patients.
引用
收藏
页码:2176 / 2180
页数:5
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