Peritoneal Mesothelioma in a Patient with Long-Standing Crohn's Disease: Cause or Coincidence?

被引:0
|
作者
Prata, Rita [1 ]
Martins, Pedro Lages [1 ]
Borges, Veronica P. [1 ]
Botelho, Pedro [2 ]
Figueiredo, Antonio [3 ]
Ramos, Jaime [1 ]
机构
[1] Unidade Local Saude Sao Jose, Dept Gastroenterol, Lisbon, Portugal
[2] Unidade Local Saude Sao Jose, Dept Colorectal Surg, Lisbon, Portugal
[3] Unidade Local Saude Sao Jose, Dept Pathol, Lisbon, Portugal
关键词
Peritoneal mesothelioma; Crohn's disease; Chronic inflammation; Mesotelioma peritoneal; Doen & ccedil; a de Crohn; Inflama & ccedil; & atilde; o cr & oacute; nica;
D O I
10.1159/000543667
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
Introdu & ccedil;& atilde;o: O mesotelioma peritoneal (PeM) & eacute; uma neoplasia prim & aacute;ria rara do revestimento peritoneal. Ao contr & aacute;rio do mesotelioma pleural, o PeM est & aacute; menos frequentemente associado & agrave; exposi & ccedil;& atilde;o a amianto. A inflama & ccedil;& atilde;o serosa cr & oacute;nica, como a que se pode observar na doen & ccedil;a de Crohn (DC), tem sido proposta como um fator que contribui para a carcinog & eacute;nese do PeM.Apresenta & ccedil;& atilde;o do caso: Homem com diagn & oacute;stico de DC ileal de longa evolu & ccedil;& atilde;o apresentou-se com epis & oacute;dios recorrentes de suboclus & atilde;o intestinal. Imagiologicamente, exibia altera & ccedil;& otilde;es sugestivas de DC ileal complexa ativa, e ascite e densifica & ccedil;& atilde;o peritoneal de novo. No intraoperat & oacute;rio, foi identificada uma massa do intestino delgado aderente ao c & oacute;lon sigmoide e n & oacute;dulos milim & eacute;tricos do peritoneu. A histologia do segmento ressecado mostrou altera & ccedil;& otilde;es compat & iacute;veis com DC e m & uacute;ltiplos focos de mesotelioma epiteli & oacute;ide, apesar da aus & ecirc;ncia de hist & oacute;ria de exposi & ccedil;& atilde;o a amianto. Foi submetido a cirurgia citorredutora combinada com quimioterapia intraperitoneal hipert & eacute;rmica, sem evid & ecirc;ncia de recidiva ap & oacute;s 15 meses de seguimento.Discuss & atilde;o/Conclus & atilde;o: Apresenta-se um caso raro de PeM n & atilde;o relacionado com exposi & ccedil;& atilde;o a amianto num doente com DC ativa de longa dura & ccedil;& atilde;o, destacando os desafios diagn & oacute;sticos e a poss & iacute;vel liga & ccedil;& atilde;o entre a inflama & ccedil;& atilde;o serosa cr & oacute;nica e o PeM.Palavras ChaveMesotelioma peritoneal, Doen & ccedil;a de Crohn, Inflama & ccedil;& atilde;o cr & oacute;nica
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页数:6
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