Aleukemic congenital leukemia cutis preceding monocytic leukemia with favorable outcome: A case report

被引:0
|
作者
Lo Presti, Caroline [1 ,4 ]
Szymanski, Gautier [1 ]
Lefebvre, Christine [1 ]
Jacob, Marie-Christine [2 ]
Mossuz, Pascal [1 ]
Gil, Hugo [3 ]
机构
[1] Grenoble Alpes Univ Hosp, Dept Biol Hematol, Grenoble, France
[2] Grenoble Alpes Univ Hosp, Dept Immunol, Grenoble, France
[3] Grenoble Alpes Univ Hosp, Dept Anatomocytopathol, Grenoble, France
[4] Inst Biol & Pathol, Hematol Biol, Blvd Chantourne, F-38700 La Tronche, France
来源
EJHAEM | 2024年 / 5卷 / 01期
关键词
acute leukemia; congenital leukemia; leukemia cutis; SPONTANEOUS REMISSION;
D O I
10.1002/jha2.861
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A newborn girl had typical "blueberry muffin" skin lesions, which shows histopathologic features of monocytic leukemia cutis. The systemic leukemia was demonstrated after one month of life. She was treated by chemotherapy, including induction and three consolidation cures, according to the ELAM02 protocol, which led to complete remission. This case report with congenital form of AML5 cutaneous localization, preceding systemic involvement, with a 5-year follow-up and positive outcome is remarkable.
引用
收藏
页码:162 / 165
页数:4
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